Amelogenesis imperfecta hypomaturative type – a rare case report

Amelogenesis imperfect (AI) is an inheritable disease manifest as enamel defect. It affects both primary and permanent dentition. It seldom affects the dentin and pulp.Amelogenesis imperfecta shows wide range of variation starting from mild discolouration to complete abrasion as soon as the teeth erupt into the oral cavity. Enamel may show quantitative as well as qualitative defect in mineral and protein content. In this article we present a special case of amelogenesis imperfecta which shows a rare hypomaturative type with sporadic inheritance and we discuss about its mode of inheritance, types, clinical presentation, histopathological features and management.