Ectodermal dysplasia relates to a group of inherited disorders where the ectodermal derivatives such as skin, sebaceous glands, hair, enamel and nails are malformed. Oligodontia or hypodontia along with abnormal shape of crown is a common dental feature of ectodermal dysplasia. There may be reduction in vertical dimension as alveolar process does not develop in absence of teeth along with varying degrees of xerostomia due to hypoplasia of salivary glands. Those cases of ectodermal dysplasia where oligodontia, abnormal shape of crown, reduced vertical height are the clinical challenges, neither removable nor fixed prosthesis is possible nor is conventional complete denture suitable. Telescopic crown with over denture can be a predictable treatment option in these cases.